Protein : CYP7A1

Name CYP7A1
Description cytochrome P450, family 7, subfamily A, polypeptide 1
Owner Public
URN urn:agi-llid:1581
Connectivity 28
Notes This gene encodes a member of the cytochrome P450 superfamily of enzymes. The cytochrome P450 proteins are monooxygenases which catalyze many reactions involved in drug metabolism and synthesis of cholesterol, steroids and other lipids. This endoplasmic reticulum membrane protein catalyzes the first reaction in the cholesterol catabolic pathway in the liver, which converts cholesterol to bile acids. This reaction is the rate limiting step and the major site of regulation of bile acid synthesis, which is the primary mechanism for the removal of cholesterol from the body. CYP7A1 is activated by PGC-1alpha. CYP7A1 polymorphism has a small but significant effect on the increase in plasma HDL cholesterol and plasma total cholesterol after an increased intake of dietary cholesterol and cafestol, respectively. CYP7A1 regulates the pathway through which cholesterol is converted into bile acids. Data reveal a fundamental difference in the regulation of CYP7A1 in rodent and human hepatocytes. Human CYP7A1 deficiency: progress and enigmas. Review. New metabolic disorder presenting with hyperlipidemia caused by a homozygous deletion mutation in CYP7A1. Present study indicates that a tight fit of cholesterol in the CYP7A1 active site is in part responsible for the high efficiency of cholesterol turnover by CYP7A1 in the liver. The liver receptor homolog-1 has emerged as an essential regulator for the expression of CYP7A1. This study has found that several kinase activators rapidly reduce the amount of bile acid produced by the human hepatoma cell line, HepG2, and that gpCYP7A1 from HepG2 cell extracts eluted in the phosphoprotein fraction of FeIII columns. Bile acids suppress transcription of the gene (CYP7A1) encoding cholesterol 7alpha-hydroxylase, the rate-limiting enzyme in bile acid biosynthesis. Characterization of the coordinated regulation of cholesterol metabolism in human liver; regulation of its mRNA in liver. Cytochrome P450, subfamily VIIA (cholesterol 7 alpha-monooxygenase), polypeptide 1. Data indicate that thyroid hormone can repress the human cholesterol 7 alpha-hydroxylase(CYP7A1) gene in transgenic mice, but this effect is dependent on gender. Data suggest that the lack of an LXR element in the region from -56 to -49 of the human CYP7A1 promoter may account for some of the differences in response to diets between humans and rodents. Demonstrated that FGF-19, acting as an FXR-induced signaling molecule, represses expression of the CYP7A1 gene; this signaling cascade defines a novel mechanism for feedback repression of bile acid biosynthesis. Dietary cholesterol regulates bile acid pool size, fecal bile acid excretion, and plasma cholesterol independently of Cyp7a1 activity. Regulation by HNF-4alpha. Regulation of CYP7A1 and CYP27A1 in human liver.
Hugo ID 2651

Microarray ID 1368458_at
j05460_s_at
1422100_at
99404_at
msa.1555.0_at
A_51_P290981
M93133
31926_at
207406_at
X56088_s_at
A_23_P146198
A_14_P132194
H378
OH0691
R619
OR0785A
T46

GenBank ID NM_007824
NP_031850
NW_047710
P18125
AAA03649
AAA40839
AAA40923
AAA41041
AAA41042
J02926
J05430
J05460
J05509
M59184
M59185
M59186
M59187
M59188
M59189
NC_005104
NM_012942
AAA58423
AAA58435
AAA61350
CAA39568
L04634
L13460
M89647
M89803
M93133
NC_000008
NM_000780
NP_000771
NT_008183
NT_086742
P22680
X56088
AAA68867
AK050020
AK050210
AK050220
AK050260
BAC34033
BAC34123
BAC34131
BAC34150
L23754
NC_000070
51467153
13787185
4503245
51467161
291937
499855
624966
180469
553228
180504
181318
181319
23908
23909
544084
34866468
7549753
7549754
203447
203448
203794
203801
203799
203792
203793
203455
203456
203204
203205
117187
26340976
5921927
51709101
31542444
31542445
797278
450622
26340741
26340742
26340921
26340922
26340937
26340938
26340975
NT_039258
Q64505
NP_037074

Chromosome position 4 A1
5q12
8q11-q12

GO ID 0004497
0005506
0005783
0005792
0006118
0006629
0006699
0006810
0008123
0008202
0008203
0016020
0020037
0046872
0016021
0016491

Alias Cholesterol 7-alpha-hydroxylase
Cholesterol 7-alpha-monooxygenase
CP7A
CYP7
Cyp7a1
CYPVII
cytochrome P450 (cholesterol hydroxylase 7 alpha)
cytochrome P450, family 7, subfamily A, polypeptide
cytochrome P450, subfamily VIIA (cholesterol 7 alpha-monooxygenase), polype
cytochrome P450, subfamily VIIA, polypeptide 1
cytochrome P450, subfamily VIIA, polypeptide I
Cytochrome P450 7A I
Cyp7a I
CYP7S I
Cytochrome P450 7A1
CHAP
Cytochrom P450 (cholesterol hydroxylase 7 alpha)
cholesterol hydroxylase 7 alpha
CYP7S1

Organism Homo sapiens
Rattus norvegicus
Mus musculus

MedLine Reference 2335522
12466851
12114517

LocusLink ID 25428
1581
13122

FunctionalClass cholesterol 7-alpha-monooxygenase
heme binding
iron ion binding
metal ion binding
monooxygenase
oxidoreductase

RGD ID 2482

Hugo Symbol CYP7A1

Unigene ID Hs.1644
Rn.10737
Mm.57029

KEGG pathway Bile acid biosynthesis

GO Cellular Component endoplasmic reticulum
membrane
microsome
integral to membrane

Cell Localization Endoplasmic reticulum

Pathway IL1B-HLA-DRB1
INS-HLA-DRB1
INS-TFRC
LEP-LRP2
PXR
PPAR all
FXR
PPARalpha
PGC1alpha
LXR
RXR
LRH-1
COUP-TF
HNF4a
NR common targets
NR CYP ABCs
NR target genes

GO Biological Process bile acid biosynthesis
cholesterol metabolism
electron transport
lipid metabolism
steroid metabolism
transport

Group Metabolic enzymes
CYPs

EC Number 1.14.13.17

MGI ID 106091

Swiss-Prot Accession P22680

OMIM ID 118455